Estimated to affected 10 million people worldwide.
Causes restrictive cardiomyopathy, with impaired filling of ventricle(s) by fibrous deposition on the endocardial surfaces.
Results from right or left heart failure or a combination of both.
Associated with heart failure associated with atrio-ventricular valve regurgitation.
Major cause of illness and death where the disease is endemic.
Estimated 2 year survival after diagnosis.
No specific treatment and its cause is poorly understood.
Most cases in the tropics, where it may be endemic.
Echocardiography standard diagnostic technique.
Poor correlation between clinical and echocardiographic findings.